Hamangioblastoma. Report a Case

Authors

Dr. med. Jorge Said Martinez (Mexico D.F., Mexico)
Dr.med. Alfonso Izita (Mexico D.F., Mexico)

Proceedings

XXXV Congress of the NES - Bad Kissingen - Germany

Topics

Neurootology
Equilibrium
Diseases
Neurootology
Equilibrium
Neurootology

Keywords

hemangioblastoma, Hipoacusia, Tinnitus, Vertigo.

Download

PDF file, 2MB

Abstract

By Definition HEMANGIOBLASTOMA is a benign tumor that may develop on the nervous system that may occur sporadically or in association with Hippel-Lindau disease. It accounts for approximately 2% of intracranial tumors, arising most frequently in the cerebellar hemispheres and vermis. Histologically, the tumors are composed of multiple capillary and sinusoidal channels lined with endothelial cells and clusters of lipid-laden pseudoxanthoma cells. Usually solitary, these tumors can be multiple and may also occur in the brain stem, spinal cord, retina, and supratentorial compartment. Cerebellar hemangioblastomas usually present in the third decade with intracranial hypertension, and ataxia. (From DeVita et al., Cancer: Principles and Practice of Oncology, 5th ed, pp2071-2)

We report  one patient with headache and symptoms of cerebellum involvement.

MRI showed a cerebellar large mass compatible with hemangioblastoma.

Often causing gradual hearing loss, tinnitus  and dizziness.If the tumor becomes large, it can interfere with the facial nerve, causing partial paralysis, and eventually pressing against brain structures, becoming life-threatening,

The diagnosis must be early, an hemangioblastoma is key to preventing its serious consequences. Unfortunately, early detection of the tumor is sometimes difficult, because the symptoms may be subtle and may not appear in the beginning stages of growth. Also, hearing loss, dizziness, and tinnitus are common symptoms of any middle and inner ear problems. Therefore, once the symptoms appear, a thorough ear examination and hearing test are essential the study the vestibular function through of vestibuloespinal, retinalocular, vestibuloocular systems in the Cranio-Corpo-Graphy (CCG), the Test of Balance(TOB) and the Computarized Electronystagmography (CNG).  in order to determine and orientate a better vestibular diagnosis. Computerized tomography(CT) and magnetic resonance imaging (MRI) are helpful in determining the location and size of a tumor and also in planning its removal.